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Blastic Plasmacytoid Dendritic Cell Neoplasm in a pediatric Peruvian patient
  • Katy Ordoñez-Tanchiva,
  • Silvana Loli-Guevara,
  • Carlos Quispe-Vicuña
Katy Ordoñez-Tanchiva
Instituto Nacional de Enfermedades Neoplasicas
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Silvana Loli-Guevara
Universidad Nacional Mayor de San Marcos Facultad de Medicina de San Fernando
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Carlos Quispe-Vicuña
Universidad Nacional Mayor de San Marcos Facultad de Medicina de San Fernando
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Abstract

Blastic plasmacytoid dendritic cell neoplasm is an aggressive and rare hematologic malignancy, exceptionally presented in children. This case reports an 11-year-old Peruvian boy, with a 2-year history of a purple-violate tumor in a leg, lymph node involvement, and histopathological study with immunohistochemistry: CD4+, CD56+, Tdt+, CD45+, TCL1+. An institutional treatment protocol for high-risk ALL was given. There was a diagnosis delay in a pediatric patient with a rare but very visible neoplasm in a low-middle income country. Despite this, the clinical course was of an indolent evolution. The institutional protocol was efficient to achieve complete oncological disease response.