Surgical management for an adult, female patient, with Ebstein Anomaly
on Tricuspid Valve that has Subvalvular membrane with severe PS and
multiple VSDs-A case report.
Ebstein’s anomaly is a rare and complexed heart defect that affects the
tricuspid valve and is accountable for around 1% of congenital cardiac
abnormalities. It is one of the most common congenital causes of
tricuspid valve regurgitation. Ebstein’s anomaly is often diagnosed
prenatally due to its severe cardiomegaly. Some individuals with this
anomaly do not experience any complications until adulthood and even
then its mostly minor complaints like exercise intolerance. Atrial
septal defect is most commonly (70-90%) associated with Ebstein’s
anomaly. However, ventricular septal defect (VSD) can be associated with
2-6% of the cases. This particular report presents a case of surgical
intervention for a 20 years old female with Ebstein’s anomaly that had
multiple VSD’s and a severe Pulmonary Stenosis (PS).