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A testicular and paratesticular localization of Desmoplastic Small Round Cell Tumor: Is it a good prognostic factor?
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  • Fabricio Romagnol,
  • Maria Teresa Alves,
  • Marília Oliveira,
  • Eny Carvalho,
  • Ana Maria da Silva,
  • Eliana Caran
Fabricio Romagnol
Federal University of Sao Paulo
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Maria Teresa Alves
Federal University of Sao Paulo
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Marília Oliveira
Federal University of Sao Paulo
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Eny Carvalho
Hospital Martagao Gesteira
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Ana Maria da Silva
Hospital Martagao Gesteira
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Eliana Caran
Federal University of Sao Paulo
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Abstract

Desmoplastic Small Round Cell Tumor (DSRCT) is an aggressive neoplasm that classically grows in peritoneal cavity and has poor prognosis. We describe a 13-year old boy with testicular DSRCT, treated with orchiectomy and chemotherapy and is free of disease 96 months after diagnosis. This is the fifth case of primary DSRCT of the testis described in literature. Moreover, we present a literature review of 28 cases of testicular and paratesticular DSRCT and discuss these locations as a prognostic factor.