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State of the Art: Evaluation and Management of Patients with Cardiac Papillary Fibroelastoma
  • John Waters,
  • Neelan Doolabh,
  • Michael Jessen
John Waters
UT Southwestern
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Neelan Doolabh
UT Southwestern
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Michael Jessen
University of Texas Southwestern Medical Center at Dallas
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Objective: To review the current literature on the state of the art of evaluation and management of cardiac papillary fibroelastoma (PFE). Methods: A literature review was performed on the topic of evaluation and management of PFE. PubWeb, Web of Science, Google Scholar, Scopus search engines were used. Key search terms included: “Cardiac papillary fibroelastoma,” “papillary fibroelastoma,” “Surgical resection of papillary fibroelastoma,” “Minimally invasive resection of papillary fibroelastoma,” “Thoracoscopy and PFE.” Relevant articles were archived and synthesized in an EndNote database. Particular attention was focused on identifying cases of minimally invasive resection of PFE and the use of thoracoscopic adjuncts to assist with cavitary PFE removal. Institutional Review Board approval was waived. Results: A total of 119 articles were identified and archived. Forty seven articles were used to compose this paper. 8 articles detailed minimally invasive resection of PFE. The largest series of minimally invasive PFE resection summed 4 patients. There are currently no guidelines to direct care of patients with PFE. General consensus is that the presence of left sided PFE should prompt evaluation for surgery. Conclusions: PFE is a rare tumor, more common in children than adults. Lesions are typically left sided and are at risk for embolization. Minimally invasive surgery is feasible and safe. Long-term outcomes with complete resection are very good.

Peer review status:IN REVISION

24 Nov 2020Submitted to Journal of Cardiac Surgery
08 Dec 2020Submission Checks Completed
08 Dec 2020Assigned to Editor
16 Dec 2020Reviewer(s) Assigned
23 Dec 2020Review(s) Completed, Editorial Evaluation Pending
27 Dec 2020Editorial Decision: Revise Major
04 Mar 20211st Revision Received
24 Mar 2021Assigned to Editor
24 Mar 2021Submission Checks Completed
05 Apr 2021Reviewer(s) Assigned
15 Apr 2021Review(s) Completed, Editorial Evaluation Pending
15 Apr 2021Editorial Decision: Revise Minor
08 Jun 20212nd Revision Received
08 Jun 2021Assigned to Editor
08 Jun 2021Submission Checks Completed
10 Jun 2021Review(s) Completed, Editorial Evaluation Pending
12 Jun 2021Editorial Decision: Revise Minor