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Flexible Bronchoscopy Findings in Children with Congenital Lobar Emphysema: 8-Year Data from a Single Center Study
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  • Gokcen Tugcu,
  • Sanem Eryılmaz,
  • Şule AKYAN SOYDAŞ,
  • Ece Ocak,
  • Murat Gençoğlu,
  • Satı Tabakçı,
  • Salih Uytun,
  • Guzin Cinel
Gokcen Tugcu
Ankara City Hospital
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Sanem Eryılmaz
Ankara City Hospital
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Şule AKYAN SOYDAŞ
Ankara City Hospital
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Ece Ocak
Ankara City Hospital
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Murat Gençoğlu
Ankara City Hospital
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Satı Tabakçı
Ankara City Hospital
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Salih Uytun
Ankara City Hospital
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Guzin Cinel
Ankara City Hospital
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Abstract

Introduction:Congenital lobar emphysema (CLE) is a rare developmental lung malformation that involves the hyperaeration of one or more lung lobes due to partial obstruction and occurs at a rate of 1/20,000–30,000 live births.Here,we aimed to retrospectively examine the clinical, radiological, and bronchoscopy findings of patients with CLE who were diagnosed and treated with surgical or conservative approaches in our clinic to compare our results with those in the literature. Method:We examined the clinical, and radiological data and FB findings of the patients with CLE aged 0–18 years at our center between 2013 and 2020.We also examined the symptoms and findings recorded during the patients’ follow-up. Results:.The median age of 20 patients with CLE at diagnosis was 3.2 years (range, 1 day–17 years).Respiratory distress and mediastinal shift were more prominent in the patients who underwent surgery than the patients who were followed up conservatively and diagnosed at an early age (p = 0.001, p = 0.049, p = 0.001, respectively). Discussion: In line with studies in the literature, the pulmonary symptoms and CLE-related imaging findings in our study regressed during the conservative follow-up.We recommend clinicians consider performing a detailed anamnesis for patients with unresolved respiratory symptoms and unilateral or bilateral increased ventilation,along with appropriate imaging tests and examinations, and should consider CLE in the diagnosis.

Peer review status:UNDER REVIEW

21 Apr 2021Submitted to Pediatric Pulmonology
22 Apr 2021Submission Checks Completed
22 Apr 2021Assigned to Editor
24 Apr 2021Reviewer(s) Assigned
10 May 2021Review(s) Completed, Editorial Evaluation Pending
15 May 2021Editorial Decision: Revise Major
24 May 20211st Revision Received
25 May 2021Submission Checks Completed
25 May 2021Assigned to Editor
25 May 2021Reviewer(s) Assigned