SURGICAL PATIENTS
Five patients underwent surgical intervention with a median age at surgery of 20 years (range 10-22). The median diameters at the time of surgery by echocardiography at the SoV was 47 mm (median Z-score: 7.2), and at the AAo was 36 mm (median Z-score: 6.4). Three out of the five patients underwent valve sparing aortic root surgery, one had aortic valve and root replacement, and one patient underwent Ross procedure. The two patients with MFS with aortic root dilation underwent valve sparing aortic root replacement. Three patients had BAV with aortic root dilation and AI. One patient with BAV underwent valve sparing aortic root replacement, one underwent Ross procedure, and the last patient had aortic valve and root replacement.