loading page

Primary osseous composite sarcoma with focal rhabdomyosarcoma and lymph node metastasis in an adolescent
  • +3
  • Maitane Andion,
  • Susana Buendía,
  • Natalia Camarena,
  • Alba Rubio-Sansimón,
  • Teresa Cañas,
  • Daniel Azorín
Maitane Andion
Hospital Niño Jesús.
Author Profile
Susana Buendía
Hospital Niño Jesús.
Author Profile
Natalia Camarena
Hospital Niño Jesús.
Author Profile
Alba Rubio-Sansimón
Hospital Infantil Universitario Niño Jesús
Author Profile
Teresa Cañas
Hospital Niño Jesús.
Author Profile
Daniel Azorín
Hospital Infantil Universitario Nino Jesus
Author Profile

Peer review status:IN REVISION

28 May 2020Submitted to Pediatric Blood & Cancer
28 May 2020Assigned to Editor
28 May 2020Submission Checks Completed
28 May 2020Reviewer(s) Assigned
15 Jun 2020Review(s) Completed, Editorial Evaluation Pending
15 Jun 2020Editorial Decision: Revise Minor

Abstract

Primary bone composite sarcoma is a very rare entity that primarily affects adolescent and young adult patients. It usually combines areas of liposarcoma and osteosarcoma and up to 60% of cases have metastatic disease at diagnosis. It is a highly aggressive pathology with intrinsic resistance to conventional treatment schemes for bone sarcomas. The prognosis is poor, with long term survival rates that do not exceed 30%. We present the case of an adolescent female diagnosed with a primary agressive bone composite sarcoma with rhabdomyosarcoma foci and loco-regional lymph node involvement.