Antiglomerular basement membrane disease is a small vessel vasculitis
which affects the lungs and kidneys, causing diffuse alveolar
haemorrhage and rapidly progressive glomerulonephritis respectively. It
is extremely uncommon in children. Diagnosis requires the presence of
specific anti-GBM autoantibodies. Presentation with renal involvement is
much more common than pulmonary involvement. However, a small proportion
of cases might have isolated pulmonary involvement. Minimal changes on
renal biopsy could still be present in these patients. Treatment of
antiglomerular basement membrane disease includes plasmapheresis and
immunosuppression. We present a case where a 7 year old boy presented
with a long history suggestive of pulmonary haemorrhage but no renal
manifestations and was diagnosed on the basis of anti-GBM autoantibodies
and renal biopsy. He responded well to immunosuppressive therapy alone.