CONCLUSIONS:
Systemic right ventricular function in patients with Senning repair was impaired at rest and during dobutamine stress echocardiography (even among asymptomatic ones) and appears to limit exercise capacity (symptom appearance), chronotropic incompetence, and increase in the severity of TV regurgitation. Right ventricular 2D echocardiography speckle tracking based global longitudinal strain (GLS) was a feasible, easy, and useful parameter in the quantitative assessment of systemic RV function in patients with Senning operation. In the children’s age group with Senning repair at peak dose DSE, the speckle based RV GLS accurately and quantitatively assessed the masked contractile reserve that was not evaluated by the ordinary volume estimation and RV ejection fraction (RV EF) methods. Despite the significant improvement in RV GLS, it did not reach the expected normal values, but it still helped estimate the masked contractile reserve thus promoted continuing cardiac anti-fibrotic treatment in these patients. Still, these children after atrial switch repair need serial long-term follow-up monitoring.