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Erdheim-Chester disease with long-standing diabetes insipidus and generalized edema
  • +4
  • Faezeh Naji,
  • Minoo Hajmiri,
  • Zahra Mazari,
  • Faeze Salahshour,
  • Vahid Soleimani,
  • Manouchehr Nakhjavani,
  • Mahboobeh Hemmatabadi
Faezeh Naji
Tehran University of Medical Sciences Endocrinology and Metabolism Research Institute

Corresponding Author:[email protected]

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Minoo Hajmiri
Tehran University of Medical Sciences Endocrinology and Metabolism Research Institute
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Zahra Mazari
Imam Khomeini Hospital Complex
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Faeze Salahshour
Imam Khomeini Hospital Complex
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Vahid Soleimani
Imam Khomeini Hospital Complex
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Manouchehr Nakhjavani
Tehran University of Medical Sciences Endocrinology and Metabolism Research Institute
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Mahboobeh Hemmatabadi
Tehran University of Medical Sciences Endocrinology and Metabolism Research Institute
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Abstract

Erdheim–Chester disease (ECD) is a rare non-Langerhans disease. This report describes a 51-year-old woman with a history of weakness, bone pain, xanthelasma palpebrarum, diabetes insipidus, and hypothyroidism. ECD is a multisystemic condition with a poor prognosis. This disease should be considered in patients with diabetes insipidus and multiorgan involvements.
04 Jul 2020Submitted to Clinical Case Reports
12 Jul 2020Submission Checks Completed
12 Jul 2020Assigned to Editor
03 Nov 2020Reviewer(s) Assigned
14 Nov 2020Review(s) Completed, Editorial Evaluation Pending
18 Jan 2021Editorial Decision: Revise Minor
15 Feb 20211st Revision Received
18 Feb 2021Assigned to Editor
18 Feb 2021Submission Checks Completed
18 Feb 2021Review(s) Completed, Editorial Evaluation Pending
29 Mar 2021Reviewer(s) Assigned
12 May 2021Editorial Decision: Revise Minor
14 Jun 20212nd Revision Received
14 Jun 2021Submission Checks Completed
14 Jun 2021Assigned to Editor
14 Jun 2021Review(s) Completed, Editorial Evaluation Pending
29 Jun 2021Reviewer(s) Assigned
12 Sep 2021Editorial Decision: Accept
Oct 2021Published in Clinical Case Reports volume 9 issue 10. 10.1002/ccr3.4898