Conclusion
  1. In the case of such tumors, not only R0 resection but also factors such as functionality and hand relief must be taken into account when making therapy decisions.
  2. The assessment of resectability must always be interdisciplinary in view of the goal, taking into account the age, localization and the biology of the tumor.
  3. A reference pathology with molecular characterization is necessary.
  4. The therapy should be done by specialized and experienced doctors in pediatriconcological surgery.
  5. Comparison with previously published data is limited, because the histological diagnoses are outdated - without the molecular genetics we can not reflect on the heterogeneity and the biology of related tumors (7;9).