Scimitar syndrome is a rare anomaly, most commonly including partial
pulmonary venous drainage into the inferior vena cava, hypoplasia of the
right lung, and systemic collaterals from the aorta. We report a
pediatric case in whom this rare syndrome was associated with
intracardiac lesions and a large aberrant systemic arterial supply to
the right lung that originated from the abdominal aorta and fistulated
in the inferior vena cava.