Introduction
Desmoplastic Small Round Cell
Tumor (DSRCT) is a rare neoplasm that affects mainly adolescent and
young adult males. This tumor presents with a polyphenotypic
differentiation profile, showing muscular, neural and epithelial markers
and carries the recurrent chromosomal translocation
t(11;22)(p13;q12)1,2 . Abdomen/pelvis are the
major sites of growth and the prognosis is poor, but data from
literature shows that patients with paratesticular DSRCT have better
outcomes2-4 . We present the fifth case of
primary DSRCT of the testis described in literature and discuss these
locations as a prognostic factor.