3.1 Clinical characteristics
Totally, 2.5% (6/237) cases with cystic lesions were confirmed
pathologically with PIE between January 2011 and April 2019 in the
Department of pathology, West China Hospital of Sichuan University. And
all the patients were treated with suggested therapy and then with
surgery.
The clinical characteristics of all the six patients are showed inTable 1 . There were four girls and two boys, ranged from 2
months to 5 years old. We collected the follow-up data of all patients
except for No.4. No.4 patient had the wrong phone number. The other
available patients (5/5, 100%) were all full-term without mechanical
ventilation. The common symptoms of the patients were cough, fever and
expectoration. All patients with PPIE were presenting as lung cysts with
primary syndrome of respiratory infection. The cystic lesion was located
at a single lobe among 66.7% (4/6) patients, who were identified with
local PPIE. 33.3% (2/6) patients affected both lung lobes, who were
identified with diffuse PPIE.
Besides, patient No.5 has suffered the disease Langerhans cell
histiocytosis (LCH) in the left submandibular lymph node for 1 year. She
was asymptomatic when she has received the suggested chemotherapy
treatment four times, she had suffered recurrent pneumonia for 3 months,
and the routine examination of the chest CT found the diffuse cystic
lesions in both lung lobes. In addition, she had the defect of
ventricular septal defect.