1. Introduction
Tumors of the heart are rare, the majority of which are metastatic tumors1. Primary cardiac tumors are extremely rare, accounting for only 0.0017%–0.19% of unselected patients at autopsy2. Seventy-five percent of them are benign neoplasms and the remainders malignant. Myxomas are by far the most common benign cardiac tumors3. As for malignant tumors arising primarily in the heart, angiosarcomas are one of the most common types4,5. Primary cardiac angiosarcoma (PCA) originates in vascular endothelial cells and commonly arises in the right atrial wall5,6. It exhibits a poor prognosis despite surgical treatment, chemotherapy, and radiotherapy1. Here, we present a case of PCA that was diagnosed for the first time at autopsy.