1. Introduction
Tumors of the heart are rare, the majority of which are metastatic
tumors1. Primary cardiac tumors are extremely rare,
accounting for only 0.0017%–0.19% of unselected patients at
autopsy2. Seventy-five percent of them are benign
neoplasms and the remainders malignant. Myxomas are by far the most
common benign cardiac tumors3. As for malignant tumors
arising primarily in the heart, angiosarcomas are one of the most common
types4,5. Primary cardiac angiosarcoma (PCA)
originates in vascular endothelial cells and commonly arises in the
right atrial wall5,6. It exhibits a poor prognosis
despite surgical treatment, chemotherapy, and
radiotherapy1. Here, we present a case of PCA that was
diagnosed for the first time at autopsy.