INTRODUCTION
Levoatrial cardinal vein (LACV) is an abnormal connection between the
left atrium or pulmonary veins and any systemic vein which is derived
from cardinal venous system (1). Most often, this anomaly has been
described in the context of left‑sided obstructive cardiac lesions such
as mitral atresia or hypoplastic left heart (2). It has been
reported to be seen together with left heart pathologies and
additionally anomalies such as double –outlet right ventricle,
tetralogy of Fallot (3), ventricular septal defect and atrioventricular
septal defect. Presence of the levoatrial cardinal vein without a
cardiac anomaly is a very rare congenital anomaly of the systemic venous
return.
In the literature, no LACV anomaly was found in two siblings who were
asymptomatic and did not have an additional cardiac anomaly. Therefore,
we present two cases ( two siblings ) the echocardiographic finding,
computed tomography (CT) and aniographic images who were diagnosed with
levoatrial cardinal vein and did not have any additional cardiac
pathology. At the same time, we wanted to share the information that
genetic tests are planned due to this rare anomaly in two siblings.