Introduction
Granulocytic sarcoma (GS) is a rare extramedullary tumor of immature myeloid cells and is frequently associated with acute or chronic leukemias [1]. GS is seen in 3% to 5% of patients with acutemyeloid leukemia (AML).When GS is associated with AML, the prognosis is very poor [2]. Certainmorphological subtypes of AML (M2,M4, M5) are more frequently associated with extramedullary myeloid tumors [3, 4]. Although most cases of GS arise synchronously with leukemias, GS may rarely be seen prior to leukemic development, and most of these cases are falsely diagnosed as lymphoma, neuroblastoma, or rhabdomyosarcoma, among others. In the pediatric age group, GS is generally localized in the orbital area, but it may also be found in the skin, bone, lymph node, and soft tissues [5]. Orbital GS, primarily a childhood disease and rarely seen in adults, is mostly observed in children under 10 years of age and is responsible for 2% to 6% of childhood orbital tumors [6–7].
In our case the tumor localization was pariatotemporal as it is not usuall presentation. By this knowledge; we presented this case report to refresh the data of granulocytic sarcoma in the literatüre and to emphasize the atypicall clinical prensentation and rare incidence.