Introduction
Granulocytic sarcoma (GS) is a rare extramedullary tumor of immature
myeloid cells and is frequently associated with acute or chronic
leukemias [1]. GS is seen in 3% to 5% of patients with
acutemyeloid leukemia (AML).When GS is associated with AML, the
prognosis is very poor [2]. Certainmorphological subtypes of AML
(M2,M4, M5) are more frequently associated with extramedullary myeloid
tumors [3, 4]. Although most cases of GS arise synchronously with
leukemias, GS may rarely be seen prior to leukemic development, and most
of these cases are falsely diagnosed as lymphoma, neuroblastoma, or
rhabdomyosarcoma, among others. In the pediatric age group, GS is
generally localized in the orbital area, but it may also be found in the
skin, bone, lymph node, and soft tissues [5]. Orbital GS, primarily
a childhood disease and rarely seen in adults, is mostly observed in
children under 10 years of age and is responsible for 2% to 6% of
childhood orbital tumors [6–7].
In our case the tumor localization was pariatotemporal as it is not
usuall presentation. By this knowledge; we presented this case report to
refresh the data of granulocytic sarcoma in the literatüre and to
emphasize the atypicall clinical prensentation and rare incidence.