INTRODUCTION
Aorto-Right Ventricular Fistula (ARVF) is a very rare condition which
communicates the ascending aorta to the cavity of the right
ventricle[1–4]. The Sinus of Valsalva fistula was
first described in 1839 and has a general incidence about 0.14% to
0.96% of all cardiac operations[3]. The structure
most frequently involved is the right coronary sinus, accounting for
64%, followed by the noncoronary sinus[1]. It’s
known that the perforation often communicates the aorta to the right
ventricle, but it can also do, rarely, to the right atrium, left
chambers or even to pericardium[1,5].
This condition is mostly like associated to ruptured aneurysm of Sinus
of Valsalva, complication of endocarditis, chest trauma, aorta
dissection or complication of another cardiac procedures as valve
replacement, Ventricular Septal Defect (VSD) correction and
Transcatheter Aortic Valve Replacement (TARV), among
others[2,6,7]. This case describes an adult with
ARVF without any of these causes above and with no other abnormalities
on the aortic valve and root, ascending aorta or ventricular septum.