PFT values (median) PFT values (median) Change per year 95% CI t P-value
Baseline End of study
FEV1 39.75% 57.8% 5.007% 3.463 to 6.552 6.356 <0.0001
FVC 41.6% 76.1% 8.212% 6.531 to 9.894 9.574 <0.0001
FEV1/FVC 90.7% 77.85% -3.537% -5.09 to -1.984 -4.464 <0.0001
MMEF25%-75% 22.2% 26.2% 1.583% 0.046 to 3.12 2.019 0.048