1 INTRODUCTION
Patients with pulmonary arterial hypertension (PAH) may develop large
pulmonary artery aneurysms (PAA) which may be complicated by rupture,
dissection or intravascular thrombus formation. These patients were
traditionally considered for heart-lung transplantation but more
recently, there have been reports of successful lung transplantation
with reconstruction of the pulmonary artery (PA).
We present two patients who underwent successful transplantation for PAH
with giant PAA using two different strategies. Furthermore, we review
previous literature and describe the treatment strategy for PAH with
PAA.