1 INTRODUCTION
Patients with pulmonary arterial hypertension (PAH) may develop large pulmonary artery aneurysms (PAA) which may be complicated by rupture, dissection or intravascular thrombus formation. These patients were traditionally considered for heart-lung transplantation but more recently, there have been reports of successful lung transplantation with reconstruction of the pulmonary artery (PA).
We present two patients who underwent successful transplantation for PAH with giant PAA using two different strategies. Furthermore, we review previous literature and describe the treatment strategy for PAH with PAA.