The authors report an exceptionally rare patient with findings of a
bicuspid aortic valve in conjunction with a mature cystic teratoma in a
middle-aged male presenting for symptomatic chest pain. Surgical
resection and valve replacement were performed, confirming the rare
cardiac tumor. While certainly interesting, this case highlights the
importance of maintaining a broad differential diagnosis and the
appropriate work-up, treatment and considerations for such rare
pathology.