Age at diagnosis [years], mean ± SD |
32.3 ± 4.9 |
Disease duration [months], median (IQR) |
94.8 (71.7) |
Active disease, n (%) |
28 (58.3) |
BDCAF, median (IQR) |
2.0 (0.0-3.0) |
Disease symptoms in patient population, n(%) |
|
Oral ulcers |
48 (100) |
Genital ulcers |
36 (75) |
Erythema nodosum |
24 (50) |
Papulopustular lesions |
28 (58.3) |
Positive pathergy test |
12 (25) |
Arthritis |
21 (43.7) |
Uveitis |
24 (50) |
Vascular involvement: |
18 (37.5) |
Venous thromobosis |
16 (89) |
Arterial aneurism |
1 (5.5) |
Pulmonary aneurism |
1 (5.5) |