4 CONCLUSION
Acalvaria is a rare fatal congenital malformation with only a few surviving cases described worldwide. We report a new surviving case with facial dysmorphia and right hemiparesis whose diagnosis was delayed. The improvement of life quality of these patients relies on the improvement of the antenatal diagnosis allowing a good planning of the delivery in order to prevent the disability linked to a probable perinatal suffering. Reporting cases of this disease allows scientists to deepen their understanding in order to find a better therapeutic strategy for these children with a vulnerable brain.