1 INTRODUCTION
Acalvaria is a rare congenital malformation characterized by the absence
of the cranial vault bones, the dura mater and associated
muscles.1 Although the basal and facial bones are
normally developed, the cranial content can often be
abnormal.1-3 Its pathogenesis is not well known, but
the abnormality occurring after neurulation is the most accepted
theory.1-3 It is a fatal condition with only a few
cases of survivors often with severe neurological
disorders.1-4 To date, only one case has been reported
in Africa.5 We report a new surviving case presenting
with facial dysmorphia and hemiparesis.