Introduction
Congenital tricuspid regurgitation (TR) is rare and represents a heterogeneous group of pathologic lesions1,2. The clinical presentation of patients with congenital TR varies based on etiology, which can occur in isolation such as Ebstein anomaly, tricuspid valve (TV) dysplasia, and TV cleft, or in association with other congenital heart defects such as atrioventricular septal defect, tetralogy of Fallot, and pulmonary stenosis with ventricular septal defect1. Even rarer, is primary isolated congenital (non-Ebstein) TR. Here, we report successful surgical tricuspid valve repair (TVr) in an asymptomatic adult with severe isolated congenital TR.