Figure Legends
Fig. 1. Fetal echocardiography at 31 weeks of gestational age. (a ) i. Single atrium and single right ventricle. ii. Narrow ascending aorta (AAo) is observed on the right side of the main pulmonary artery. iii. Color Doppler image of (a)-ii. (b ) i. An abnormal pulmonary vein (PV) is behind the single atrium (dotted arrow). ii/iii. Left PV blood flow runs off to the right side at increased flow velocity. (c ) i. Doppler wave form in the right PV is rich and biphasic. ii. Doppler wave form in the left PV is non-pulsatile continuous flow. (d ) Axial single-shot spin echo magnetic resonance image at 35 weeks of gestational age. Bilateral lungs are heterogeneous without nutmeg lung pattern. DAo, descending aorta; LSVC, left superior vena cava; mPA, main pulmonary artery.
Fig. 2. Computed tomography angiography with three-dimensional reconstruction. (a ) Pulmonary window setting. Severe pulmonary congestion in the left lung. (b ) The right pulmonary vein (PV) entered the left superior vena cava (LSVC). (c ) Anterior-posterior image of three-dimensional reconstruction. An extremely narrow ascending aorta (AAo) is observed. (d ) Posterior-anterior image. The right PV enters the right superior vena cava (SVC) without stenosis. The left PV enters the LSVC with stenosis. Bilateral PVs have communication by a tortuous vessel.