Figure Legends
Fig. 1. Fetal echocardiography at 31 weeks of gestational age.
(a ) i. Single atrium and single right ventricle. ii. Narrow
ascending aorta (AAo) is observed on the right side of the main
pulmonary artery. iii. Color Doppler image of (a)-ii. (b ) i. An
abnormal pulmonary vein (PV) is behind the single atrium (dotted arrow).
ii/iii. Left PV blood flow runs off to the right side at increased flow
velocity. (c ) i. Doppler wave form in the right PV is rich and
biphasic. ii. Doppler wave form in the left PV is non-pulsatile
continuous flow. (d ) Axial single-shot spin echo magnetic
resonance image at 35 weeks of gestational age. Bilateral lungs are
heterogeneous without nutmeg lung pattern. DAo, descending aorta; LSVC,
left superior vena cava; mPA, main pulmonary artery.
Fig. 2. Computed tomography angiography with three-dimensional
reconstruction. (a ) Pulmonary window setting. Severe pulmonary
congestion in the left lung. (b ) The right pulmonary vein (PV)
entered the left superior vena cava (LSVC). (c )
Anterior-posterior image of three-dimensional reconstruction. An
extremely narrow ascending aorta (AAo) is observed. (d )
Posterior-anterior image. The right PV enters the right superior vena
cava (SVC) without stenosis. The left PV enters the LSVC with stenosis.
Bilateral PVs have communication by a tortuous vessel.