INTRODUCTION:
The word teratoma is derived from the Greek word ’teratos,’ which means a monster. The most common benign lesion in young women is a mature cystic teratoma. Malignant transformation is rare and seen in less than 3% of the cases [1]. The chances of malignant transformation increase with age and are most common in post-menopausal women of the 4th to 5th decade [2]. Mature cystic teratoma of the ovary (MCTO) can transform into squamous cell carcinoma, adenocarcinoma, and papillary carcinoma, squamous cell carcinoma being the most common. Previous studies have shown a poor prognosis for the malignant transformation of MCTO [3]. It is nearly impossible to diagnose the malignant transformation of MCTO preoperatively due to the tumor’s rarity and its similarity to MCTO [4].
Furthermore, due to the condition’s rarity, no standard treatment has been established for its management yet. There are several studies of malignant transformation of MCTO; however, undifferentiated carcinoma arising in the MCTO is exceedingly rare. Here, we present a rare case of undifferentiated carcinoma arising from MCTO.