Introduction
Coronary artery anomalies are relatively uncommon congenital disorders
of the coronary artery anatomy. The incidence of coronary artery
anomalies has been reported to be 0.6–1.3%. [1] Left main coronary
artery atresia (LMCAA) is the rarest form of congenital coronary
malformations, in which coronary ostium and main trunk in the left
coronary artery system is absent [2]. Thus, blood flows from the
right coronary artery to the left coronary artery through collateral
vessels [3]. Clinical presentation, management, and prognosis of
this disease depend on the characteristics of the collaterals and native
vessels [4]. Hereby, we report a case of congenital atresia of the
left main coronary artery, misdiagnosed as Anomalous left coronary
artery from the pulmonary artery (ALCAPA).