Abstract
Enlargement of the aorta is a severe sequela of tetralogy of Fallot (TOF) that can cause fatal complications including aortic regurgitation, dissection, aneurysm or even rupture. Valve sparing aortic root replacement (VSARR), also known as the Yacoub technique, is a surgical maneuver that corrects regurgitation and avoids requirement for long-term anticoagulation treatment at the same time. Several studies have demonstrated the effectiveness of VSARR in patients with aortic regurgitation complicated by aortic root dilation following a repair of congenital heart defects. To date, little data exists on VSARR in TOF patients. Herein we report a case of a previously unoperated 35-year-old male TOF patient. He was admitted due to dyspnea, initial physical examination demonstrated cyanosis and heart murmurs. Echocardiography suggested secundum atrial septal defect, perimembranous ventricular septal defect and mild-severe aortic regurgitation. Computed tomography angiography indicated aortic root dilation and suspicious right coronary artery aneurysm. Concurrent repair of TOF and VSARR was performed successfully and the patient had a satisfactory recovery.
KEYWORDS: Aortic root replacement; Congenital heart disease; Tetralogy of Fallot