1 | INTRODUCTION
Enlargement of the aorta is a severe sequela of tetralogy of Fallot (TOF), which can lead to fatal outcomes like aortic regurgitation (AR), dissection, aneurysm, or even rupture with fatal consequences, even in those patients who have had a repair of TOF.[1] Valve sparing aortic root replacement (VSARR), also known as the Yacoub technique, is a surgical procedure that has the advantages of correcting AR, preserving native aortic valves, avoiding prosthetic valves and subsequent requirement for long-term anticoagulation treatment.[2] Several studies have demonstrated the effectiveness of VSARR in patients with AR complicated by aortic root dilation following a repair of congenital heart defects.[2, 3] To date, VSARR has not been performed on TOF patients undergone no intervention. Here we described a case of a previously unoperated TOF patient undergoing VSARR and concurrent repair of TOF successfully.