Sex
Age (years)
Second CFTR variant
Symptoms at study end
Last SC
Final Diagnosis
M 27 F1052V Bronchiectasis; CBAVD; Pa chronic detection 62 CF
F 5 S1455X HA 112 CF
M 18 5T;TG12 Pancreatitis 55 CFTR-RD
F 16 5T;TG12 33 CFTR-RD
F 15 5T;TG12 HA 20 CFTR-RD
M 12 D1152H HA 10 CFTR-RD
M 3 5T;TG12 46 CFTR-RD
M 14 D579G 50 CFTR-RD
F 47 5T;TG12 19 CFTR-RD
M 47 5T;TG12 CBAVD 31 CFTR-RD
F 11 5T;TG12 11 CRMS/CFSPID
M 8 R74W;D1270N 12 CRMS/CFSPID
F 7 5T;TG12 14 CRMS/CFSPID
F 6 R74W;D1270N 14 CRMS/CFSPID
F 6 5T;TG12 35 CRMS/CFSPID
F 6 5T;TG12 25 CRMS/CFSPID
F 5 5T;TG12 13 CRMS/CFSPID
M 4 5T;TG12 12 CRMS/CFSPID
M 3 D1152H 19 CRMS/CFSPID
M 3 L967S 10 CRMS/CFSPID
M 2 D1152H 42 CRMS/CFSPID
F 7 D1152H 58 CRMS/CFSPID
F 4 D1152H HA 26 CRMS/CFSPID
M 1 D1152H 42 CRMS/CFSPID
F 3 Y1032C 35 CRMS/CFSPID
F 2 R117H;7T 32 CRMS/CFSPID
M 8 R117H;7T 27 CRMS/CFSPID