Case:
A 17 year old female presented with 4 months history of progressive abdominal distension associated with abdominal pain, yellowing discoloration of eyes, and on and off constipation. Abdominal CT-scan showed a huge cystic mass in the right upper quadrant extending inferiorly to the right lumbar region. Complete cyst excision of type IA was done plus Cholecystectomy in addition to bilioenteric reconstruction.