Demographic / clinical characteristic |
Value |
Sex (M/F) |
22/35 |
ΔF508 homozygous (%) |
15 |
ΔF508 heterozygous (%) |
85 |
Age (yrs) ± SD |
18.56 (8.54) |
Height (cm) ± SD |
150.16 (20.63) |
Weight ± SD |
46.11 (16.87) |
BMI ± SD |
19.69 (3.49) |
Chronic pseudomonas aeruginosa colonization (%) |
44% |
Pancreatic insufficiency (%) |
96.5 % |
Patients on CFTR modulator (%) |
17 % |