List of abbreviations:
Multiple Breath washout (MBW)
Cystic Fibrosis (CF)
Lung clearance index (LCI)
Forced expiratory volume in 1 second (FEV1)
Cystic fibrosis transmembrane conductance regulator (CFTR)
Pulmonary exacerbation (PE)
Intravenous (IV)
Forced vital capacity (FVC)
Forced expiratory flow 25–75% (FEF25-75)
Pediatric and Pre-adult age (PPaa)