Demographic / clinical characteristic Value
Sex (M/F) 22/35
ΔF508 homozygous (%) 15
ΔF508 heterozygous (%) 85
Age (yrs) ± SD 18.56 (8.54)
Height (cm) ± SD 150.16 (20.63)
Weight ± SD 46.11 (16.87)
BMI ± SD 19.69 (3.49)
Chronic pseudomonas aeruginosa colonization (%) 44%
Pancreatic insufficiency (%) 96.5 %
Patients on CFTR modulator (%) 17 %