Sex Male – n (%) |
19 (54,3) |
Age (years) – median (SD) |
12,04 (4,0) |
CFTR mutation – n (%)
F508del/F508del
F508del/other
Other/other
|
13 (37,1)
15 (42,9)
7 (20)
|
BMI (kg/m2) – median (SD) |
16,38 (2,11) |
FEV1pp (%)* – median (SD) |
90,81
(16,71) |
Pancreatic insufficiency – n (%) |
31 (88,6) |
Liver disease related to CF – n (%) |
14 (40) |
Diabetes related to CF – n (%) |
2 (5,7) |
History of ABPA – n (%) |
3 (8,6) |
History of hemoptysis – n (%) |
1 (2,9) |
Respiratory support – n (%) |
0 (0) |
Chronic airway infection-colonization**– n (%)
Pseudomonas aeruginosa
Methicillin-sensitive Staphylococcus aureus
Methicillin-resistant Staphylococcus aureus
Mycobacterium abscessus
Burkholderia cenocepacia
|
6 (17,1)
19 (54,3)
0 (0)
0 (0)
1 (2,9)
|