Sex Male – n (%) 19 (54,3)
Age (years) – median (SD) 12,04 (4,0)
CFTR mutation – n (%) F508del/F508del F508del/other Other/other 13 (37,1) 15 (42,9) 7 (20)
BMI (kg/m2) – median (SD) 16,38 (2,11)
FEV1pp (%)* – median (SD) 90,81 (16,71)
Pancreatic insufficiency – n (%) 31 (88,6)
Liver disease related to CF – n (%) 14 (40)
Diabetes related to CF – n (%) 2 (5,7)
History of ABPA – n (%) 3 (8,6)
History of hemoptysis – n (%) 1 (2,9)
Respiratory support – n (%) 0 (0)
Chronic airway infection-colonization**– n (%) Pseudomonas aeruginosa Methicillin-sensitive Staphylococcus aureus Methicillin-resistant Staphylococcus aureus Mycobacterium abscessus Burkholderia cenocepacia 6 (17,1) 19 (54,3) 0 (0) 0 (0) 1 (2,9)