Introduction
In 1971 Gianotti et al. first described benign cephalic histiocytosis
(BCH) and up to the present approximately 70 cases have been reported in
the literature. (1, 2) BCH belongs to the group of non-Langerhans cell
histiocytoses (NLCH) and clinically and histologically resembles
juvenile xanthogranuloma (JXG) and generalized eruptive histiocytosis
(GEH). Skin lesions are characterized by erythematous, yellowish to
brownish macules and papules, which are mostly located on head and neck.
The etiology of BCH is as yet unresolved.