loading page

Congenital superior vena cava (SVC) stenosis and obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) - A surgical perspective
  • +2
  • Sachin Mahajan,
  • Sudhansoo Khanna,
  • Manojkumar Rohit,
  • Nirupam Chakraborty,
  • Ankit Singhal
Sachin Mahajan
Post Graduate Institute of Medical Education and Research
Author Profile
Sudhansoo Khanna
Post Graduate Institute of Medical Education and Research
Author Profile
Manojkumar Rohit
Post Graduate Institute of Medical Education and Research
Author Profile
Nirupam Chakraborty
Post Graduate Institute of Medical Education and Research
Author Profile
Ankit Singhal
Post Graduate Institute of Medical Education and Research
Author Profile

Abstract

Congenital superior vena cava (SVC) stenosis is a very rare anomaly especially in pediatric population. Co-existence with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) has never been reported. Clinical examination should prompt detailed and focused evaluation for this treatable etiology. SVC stenosis, although causing SVC syndrome, may decrease the severity of pulmonary venous hypertension by limiting the amount of blood in obstructed common chamber. Pericardial patch augmentation can cure SVC stenosis, and may allow for growth potential as well. We describe a case of congenital SVC stenosis in a case of obstructed supra-cardiac TAPVC in a 3 month old infant, managed successfully.

Peer review status:ACCEPTED

19 Apr 2020Submitted to Journal of Cardiac Surgery
20 Apr 2020Assigned to Editor
20 Apr 2020Submission Checks Completed
23 Apr 2020Reviewer(s) Assigned
01 May 2020Review(s) Completed, Editorial Evaluation Pending
12 Jun 2020Editorial Decision: Accept