Abstract
Abstract: Paediatric pancreatic tumours by virtue of their rarity pose a
significant challenge for the management.1 Although pancreatoblastoma
and acinar cell carcinoma are distinct tumour entities, there is
considerable overlap of histopathological characteristics which makes
the diagnosis difficult pathologically.2 In infancy and childhood
pancreatoblastoma is the most common tumour.3 Acinar cell carcinoma
usually presents in older children.4,5 We describe a four year old child
with acinar cell carcinoma which is possibly only the fourth case with
this condition at such a young age.