BACKGROUND Isolated left upper partial anomalous pulmonary venous connection (PAPVC) via innominate vein to the right atrium with intact atrial septum is a rare congenital anomaly. Diagnosis requires a high degree of suspicion, otherwise it may remain undetected. This study was undertaken to determine the efficacy of a modified suprasternal view in transthoracic echocardiography (TTE) for the detection of left upper PAPVC. METHODS After diagnosis of left upper PAPVC in our first patient incidentally in 2008, we have added the modified suprasternal view to all TTEs performed in our pediatric cardiology clinic. This was obtained by tilting the tail of the probe 30-45 degrees towards the right shoulder of the patient during suprasternal long axis for a better view of the innominate vein and search for left upper PAPVC. RESULTS Among 7200 patients who underwent TTEs between 2008-2020, we have identified 13 patients with left upper PAPVC into the innominate vein by using our modified suprasternal approach. All were asymptomatic children, aged between 5 months and 16 years. In all patients, cardiac chambers were normal in size and there were no accompanying congenital disorders. In 10 cases, diagnoses were confirmed by multi-slice computerized tomography, whereas one patient underwent catheterization for confirmation. CONCLUSION Isolated left upper PAPVC to innominate vein with intact atrial septum is a rare congenital disorder and can be present in asymptomatic children with normal cardiac chambers. TTE, with a modified approach in suprasternal long axis view, has a high diagnostic value in the detection of this condition

Left atrial appendage aneurysm (LAAA) is a rare congenital anomaly which can be associated with cardiovascular morbidity and mortality by predisposing to atrial tachyarrhythmias, thromboembolism and cardiac failure. In this case report a patient presenting with supraventricular arrythmias and chest pain due to LAAA is presented. Surgical treatment was performed through median sternotomy with cardiopulmonary bypass through which the giant aneurysm of the left atrial appendage, extending to the apex of the left ventricle was surgically managed successfully. Surgical treatment is curative and proposed as the main treatment modality regardless of the presence or absence of symptoms.

Abstract The life expectancy and quality of patients with complete atrioventricular septal defect (CAVSD), which has undergone significant modifications in surgical correction since its definition, are increasing. Materials and Methods A total of 56 patients with a median age of 9 months were operated in the last 10 years. The modified single-patch (MSP) and two-patch technique (TPT) were applied to 37 patients and 19 patients, respectively. The patients were compared in terms of the ventricular septal defect (VSD) diameter, cardio pulmoner bypass (CPB) and aortic cross-clamp (ACC) time, intubation time, length of intensive care unit (ICU) in addition to demographic and hospital data. Long term results of 45 patients have been evaluated for 73,2 ± 4,06 months meanly. Results It was observed that the age distribution of the patients who underwent MSP was lower (p=0.003), and were more female patients (p=0.023). The VSD diameter was larger in the TPT (p=0.000). The right atrioventricular valve (RAVV) repair was observed significantly more in the MSP technique (p=0.043). CPB and ACC time were found to be significantly longer in the TPT technique according to the T-test result. While postoperative LAVV regurgitation was found to be lower in the MSP (p=0.016), the amount of drainage was higher in the TPT. No statistical significance was detected in other comparative values of early and the long term results of the both tecniques. Conclusion In this retrospective study, it was observed that the MSP was advantageous in surgical outcomes, its easier applicability in accordance with the literature.